Langerhansian histiocytosis (LH) is a group of disorders characterized by tissue infiltration by Langerhans cells or dendritic cells originating from the reticuloendothelial system and organized in granulomas. The Langerhansian nature of the disease is confirmed by immunohistochemistry, with expression of CD1a or langerin/CD207, or by electron microscopy, with the presence of Birbeck granules 1,2].It is a rare disease that mainly affects children...